Sprengel Deformity with Cervical Myelopathy a Rare Entity: A Case Report

Sharif Al Qadhi¹, Neeraj Salhotra^2, , Bashar Al Tunbi³, C. Livingston³, Fahad Al Kheder³, Mohammad Hashim⁴ and Kauthar Al Zakwani⁴

¹Consultant neurospine surgeon Khoula hospital Muscat

²Consultant neurosurgeon Khoula hospital Muscat

³Specialist neurosurgeon Khoula hospital Muscat

⁴Medical officer neurosurgeon Khoula hospital Muscat

Cite this paper:
Sharif Al Qadhi, Neeraj Salhotra, Bashar Al Tunbi, C. Livingston, Fahad Al Kheder, Mohammad Hashim and Kauthar Al Zakwani. Sprengel Deformity with Cervical Myelopathy a Rare Entity: A Case Report. American Journal of Medical Case Reports. 2021; 9(12):702-704. doi: 10.12691/ajmcr-9-12-10

Abstract

Sprengel's Deformity is a congenital condition characterized by a small and undescended scapula often associated with scapular winging and scapular hypoplasia. Diagnosis is made clinically with a high-riding, medially rotated, triangular-shaped scapula, with associated limitations in shoulder abduction and flexion. Treatment is observation in the absence of shoulder dysfunction. Operative management is indicated in the presence of severe cosmetic concerns or functional deformities (abduction < 110-120 degrees). We herewith present a case of this deformity seen in our center in patient of cervical stenosis with myelopathy.

Keywords:
Sprengel deformity cervical myelopathy scapular winging

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References:

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