Recurrent Still’s Disease

Irvind Buttar^1, , Elizabeth McCuaig¹, Harry Fischer² and Erin Patton²

¹Internal Medicine, Northwell Health/Lenox Hill Hospital, New York, United States

²Rheumatology, Northwell Health/Lenox Hill Hospital, New York, United States

Cite this paper:
Irvind Buttar, Elizabeth McCuaig, Harry Fischer and Erin Patton. Recurrent Still’s Disease. American Journal of Medical Case Reports. 2022; 10(10):274-276. doi: 10.12691/ajmcr-10-10-6

Abstract

Adult-onset Still’s disease (AOSD) is a systemic inflammatory disorder. Its clinical presentation is similar to the systemic form of Juvenile idiopathic arthritis (JIA). In this case report we explore a young female 22 years after a diagnosis of JIA and 4 years after her diagnosis of AOSD who presents with systemic inflammatory symptoms. Some of the symptoms consistent with her previous diagnosis and some new. Specifically the new symptom of her diffuse lymphadenopathy lead to a differential of possible lymphoproliferative disease. After a biopsy and multiple admissions with unrelenting symptoms the patient was diagnosed with a flare of AOSD. We explore her case in depth with the question in mind: Does one diagnosed with JIA remain on long term therapy to avoid recurrent flares and progression to AOSD, and if so for how long?

Keywords:
stills disease juvenile idiopathic arthritis lymphadenopathy

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