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M. Yamaguchi, A. Ohta, T. Tsunematsu et al., “Preliminary criteria for classification of adult Still's disease,” Journal of Rheumatology, vol. 19, no. 3, pp. 424-430, 1992.

has been cited by the following article:

Article

Recurrent Still’s Disease

1Internal Medicine, Northwell Health/Lenox Hill Hospital, New York, United States

2Rheumatology, Northwell Health/Lenox Hill Hospital, New York, United States


American Journal of Medical Case Reports. 2022, Vol. 10 No. 10, 274-276
DOI: 10.12691/ajmcr-10-10-6
Copyright © 2022 Science and Education Publishing

Cite this paper:
Irvind Buttar, Elizabeth McCuaig, Harry Fischer, Erin Patton. Recurrent Still’s Disease. American Journal of Medical Case Reports. 2022; 10(10):274-276. doi: 10.12691/ajmcr-10-10-6.

Correspondence to: Irvind  Buttar, Internal Medicine, Northwell Health/Lenox Hill Hospital, New York, United States. Email: ibuttar1@northwell.edu

Abstract

Adult-onset Still’s disease (AOSD) is a systemic inflammatory disorder. Its clinical presentation is similar to the systemic form of Juvenile idiopathic arthritis (JIA). In this case report we explore a young female 22 years after a diagnosis of JIA and 4 years after her diagnosis of AOSD who presents with systemic inflammatory symptoms. Some of the symptoms consistent with her previous diagnosis and some new. Specifically the new symptom of her diffuse lymphadenopathy lead to a differential of possible lymphoproliferative disease. After a biopsy and multiple admissions with unrelenting symptoms the patient was diagnosed with a flare of AOSD. We explore her case in depth with the question in mind: Does one diagnosed with JIA remain on long term therapy to avoid recurrent flares and progression to AOSD, and if so for how long?

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