American Journal of Medical Case Reports
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American Journal of Medical Case Reports. 2022, 10(3), 45-47
DOI: 10.12691/ajmcr-10-3-1
Open AccessCase Report

Pauci-immune Crescentic Glomerulonephritis: Case Report

Wisam Mnkana1, Nikita Wong2, Eman EL-Sawalhy1, , Ahmed Abdelrahim1, Hussein Gaith1, Zhang Ping3 and Rabih Bazzi4

1Department of Internal Medicine, Beaumont Hospital, Dearborn, MI

2Wayne State University, School of Medicine, Detroit, MI

3Pathology Department, Oakland University William Beaumont School of Medicine

4Division of Nephrology, Internal Medicine Department, Beaumont Hospital, Dearborn, MI

Pub. Date: March 01, 2022

Cite this paper:
Wisam Mnkana, Nikita Wong, Eman EL-Sawalhy, Ahmed Abdelrahim, Hussein Gaith, Zhang Ping and Rabih Bazzi. Pauci-immune Crescentic Glomerulonephritis: Case Report. American Journal of Medical Case Reports. 2022; 10(3):45-47. doi: 10.12691/ajmcr-10-3-1

Abstract

Pauci-immune glomerulonephritis ( PIGN) is a potentially life-threatening condition that progresses rapidly to renal failure within days or weeks. Here we present a 62 -year-old African American female who was found to have acute kidney injury at the time of presentation. Further workup including renal biopsy showed anti-neutrophilic cytoplasmic antibodies (ANCA) associated pauci-immune crescentic glomerulonephritis. The patient was started on steroids and cyclophosphamide however, the patient’s kidney function continued to get worse and required hemodialysis. Unfortunately, our patient passed away after two months of diagnosis secondary to cardiac arrest.

Keywords:
Pauci immune glomerulonephritis crescentic glomerulonephritis survival

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