Arteriovenous Malformation in CLOVES Syndrome

Laith Alkukhun¹, Ahmed Abu-Haniyeh^1, , Mohammed Al-natour², Muhammad Hassan³ and Adriano Tonelli⁴

¹Internal Medicine Residency Program, Medicine Institute, Cleveland Clinic, Cleveland, OH, USA

²Interventional Radiology Department, Imaging Institute, Cleveland Clinic, Cleveland OH, USA

³Jinnah Sindh Medical University, Karachi, Pakistan

⁴Department of Pulmonary, Allergy and Critical Care Medicine, Respiratory Institute, Cleveland Clinic, OH, USA

Cite this paper:
Laith Alkukhun, Ahmed Abu-Haniyeh, Mohammed Al-natour, Muhammad Hassan and Adriano Tonelli. Arteriovenous Malformation in CLOVES Syndrome. American Journal of Medical Case Reports. 2017; 5(6):160-162. doi: 10.12691/ajmcr-5-6-7

Abstract

CLOVES syndrome (Congenital Lipomatous Overgrowth, Vascular malformations, and Epidermal nevi) is a rare and recently discovered syndrome. It is associated with vascular malformations and abnormal fatty tissue and skeletal growth. In this case, we report the clinical manifestations overtime in a patient with CLOVES syndrome who presented a unique arteriovenous malformation that led to severe neurological impairment by compressing the spinal cord. We also discuss the visceral findings in our patient, such as double ureter and splenomegaly, and describe the finding of corneal hydrops in both eyes and Chiari I malformation on brain imaging.

Keywords:
CLOVES syndrome arteriovenous malformation disseminated intravascular coagulation

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