ROSAI DORFMAN SYNDROME- A RARE CASE REPORT IN AN ASIAN MALE

Kulkarni Sweta¹, Ramesh R¹, Ruben Toi¹, Wilma Delphine Silvia CR² and Suruthi Meenakshi¹

¹Department of Biochemistry, Mahatma Gandhi Medical College & Research Institute, Pondicherry.

²Department of Biochemistry, Akash Institute of Medical Sciences & Research & Centre, Bangalore.

Cite this paper:
Kulkarni Sweta, Ramesh R, Ruben Toi, Wilma Delphine Silvia CR and Suruthi Meenakshi. ROSAI DORFMAN SYNDROME- A RARE CASE REPORT IN AN ASIAN MALE. International Journal of Clinical and Diagnostic Research. 2017; 5(1):1-5. doi: 10.12691/ijcdr-5-1-1

Abstract

Rosai–Dorfman disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a benign, self-limited, idiopathic proliferative histiocytic disorder originally described by Destombes in 1965 and later in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with fever, polyclonal gammopathy and leukocytosis with neutrophilia. The skin is the most common site affected. Extranodal manifestations have been reported in 43% of cases. In the present case report a young male from Asian origin diagnosed to be suffering from RDD is discussed.

Keywords:
Histiocytosis Emperipolesis Gammopathy Neutrophilia

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