A Dento – Surgical Management of a Cleidocranial Dysplasia Case. A New Approach for Better Oral Health Quality of Life Part II to: (A 9-year-old Saudi Boy with Cliedocranial Dysplasia)

Rabab A. Al Buainain¹, Tarek Ezzeldin², Hoda Abougareeb³, Faisal Al Sineedi⁴, Basma A. Almaghlouth⁵, Yousef H. Almoumen⁶ and Abdullah Faraj Alshammari^7,

¹Senior Resident in Saudi Board Pediatric Dentistry Program, Dammam Medical Complex, Ministry of Health, Kingdom of Saudi Arabia

²Consultant in Pediatric Dentistry, (French Board Certified) Dammam Medical Complex, Ministry of Health, Kingdom of Saudi Arabia

³Consultant in Pediatric Dentistry, Dammam Medical Complex, Ministry of Health, Kingdom of Saudi Arabia

⁴Consultant in Pediatric Dentistry, King Fahad Military Medical Complex, Ministry of Defense, Kingdom of Saudi Arabia

⁵SBO Consultant in Orthodontics, Dammam Medical Complex, Ministry of Health, Kingdom of Saudi Arabia

⁶Consultant in Oral & Maxillo Facial Surgery, BDS, SBOMFS, AAAM (American Academy of Aesthetic Medicine Board Certified)

⁷College of Dentistry, University of Hail, Hail, KSA

Cite this paper:
Rabab A. Al Buainain, Tarek Ezzeldin, Hoda Abougareeb, Faisal Al Sineedi, Basma A. Almaghlouth, Yousef H. Almoumen and Abdullah Faraj Alshammari. A Dento – Surgical Management of a Cleidocranial Dysplasia Case. A New Approach for Better Oral Health Quality of Life Part II to: (A 9-year-old Saudi Boy with Cliedocranial Dysplasia). American Journal of Medical Case Reports. 2018; 6(10):193-201. doi: 10.12691/ajmcr-6-10-1

Abstract

Background: Cleidocranial dysplasia is a rare congenital defect of autosomal dominant heritable disease with prevalence of 1 per 1,000000 individuals. It is primarily affects bones which undergo intramembranous ossification [1,2,3,4]. Case presentation: A 9 years old Saudi male with CCD attended Pediatric Dental Clinics in Dammam Medical Complex. Chief complaint was delay eruption of permanent teeth and multiple caries. Based on clinical examination, radiographic investigations including CBCT & with coordination between Pediatric Dentistry, maxillofacial surgery and Orthodontic departments, a treatment plan has been concluded taking into consideration the wellbeing and the oral health related life style of the patient by addressing a new approach to preserve all the primary teeth, surgically removing all supernumerary teeth, applying removal or fixed modified Gropers’ appliance to improve speech, esthetic & function than observing the eruption of the permanent teeth to intervene orthodontically only when needed. Conclusion: Team work involving multi-disciplinary departments helped to select a preeminent & new dental management approach for CCD patients including all aspects needed, Dental rehabilitation, Surgical & Orthodontic treatment to provide better oral health quality of life for the young patient.

Keywords:
cliedocranial dysplasia dammam approach oral health quality of life dento-surgical management

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