Atypical Cogan's Syndrome: Case Report of an Oculoaudiovestibular Disease

Btissaam. Belhoucha^1, , S Belghmidi², I. Benbaddan³, Youssef. Rochdi¹, I Hajji², Hassan. Nouri¹, lahcen. Aderdour¹, M. Hattaoui³, A Moutaouakil² and Abdelaziz. Raji¹

¹Department of ENT, CHU Med VI, Marrakech 2360, Morocco

²Department of ohtalmology, CHU Mohammed VI, Marrakech, Maroc

³Department of cardiology, CHU Mohammed VI, Marrakech, Maroc

Cite this paper:
Btissaam. Belhoucha, S Belghmidi, I. Benbaddan, Youssef. Rochdi, I Hajji, Hassan. Nouri, lahcen. Aderdour, M. Hattaoui, A Moutaouakil and Abdelaziz. Raji. Atypical Cogan's Syndrome: Case Report of an Oculoaudiovestibular Disease. American Journal of Medical Case Reports. 2014; 2(7):139-142. doi: 10.12691/ajmcr-2-7-3

Abstract

Cogan's syndrome (CS) is a rare autoimmune vasculitis. Clinical hallmarks are bilateral interstitial keratitis and vestibuloauditory dysfunction. Association between Cogan's syndrome and systemic vasculitis as well as aortitis also exists. We report a case of cogan’s syndrome in 12 year old girl who intialy present with bilateral interstitial keratitis with audiovestibular and cardiac symptoms. We discuss the clinical aspect, the pathogenic mechanisms, the laboratory investigations, the differential diagnosis and traitement of cogan syndrome.

Keywords:
cogan’s syndrome interstitial keratitis deafness

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