Quadricuspid Aortic Valve: A Case Report and Review

Pramod Theetha Kariyanna¹, Jonathan Francois¹, Amog Jayarangaiah², Yuvraj Singh Chowdhury¹, Richard Grodman³, Moro O. Salifu¹ and Isabel M. McFarlane^1,

¹Department of Internal Medicine, State University of New York, Downstate Medical Center, Brooklyn NY 11203, USA

²Trinity School of Medicine, Ratho Mill, Ribishi, St. Vincent and Grenadines

³Richmond University Medical Center, Department of Cardiology, Staten Island, New York, United States

Cite this paper:
Pramod Theetha Kariyanna, Jonathan Francois, Amog Jayarangaiah, Yuvraj Singh Chowdhury, Richard Grodman, Moro O. Salifu and Isabel M. McFarlane. Quadricuspid Aortic Valve: A Case Report and Review. American Journal of Medical Case Reports. 2020; 8(8):253-256. doi: 10.12691/ajmcr-8-8-11

Abstract

Quadricuspid aortic valve (QAV) is a rare congenital valvular abnormality with less than 200 cases reported to date. The first QAV was reported in 1862 by Balington. Clinical manifestations of patients with a QAV depend on the functional status of the QAV and the associated cardiac disorders. Most QAV are asymptomatic and are incidentally found. Severe aortic regurgitation and/or stenosis can develop overtime, requiring aortic valve replacement or repair. Transesophageal echocardiography is the preferred modality to diagnose QAV. We present a case of QAV which was incidentally diagnosed in a 43-year-old woman who presented with gastroenteritis.

Keywords:
Quadricuspid aortic valve congenital variant of aortic valve Hurwitz and Robert’s classification

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