Portopulmonary Hypertension with Liver Cirrhosis

Tyler Kemnic^{1, 2,} , James Choi^{1, 2}, Manel Boumegouas^{1, 2} and Shaurya Srivastava³

¹Michigan State University Department of Medicine

²Sparrow Hospital

³Michigan State University College of Osteopathic Medicine

Cite this paper:
Tyler Kemnic, James Choi, Manel Boumegouas and Shaurya Srivastava. Portopulmonary Hypertension with Liver Cirrhosis. American Journal of Medical Case Reports. 2020; 8(5):137-139. doi: 10.12691/ajmcr-8-5-7

Abstract

A 49-year-old male with a past medical history of smoking (20 pack-years), 25 years of daily drinking, type 2 diabetes, alcoholic liver cirrhosis, hyperlipidemia, and hypertension presented with a complaint of weakness, shortness of breath and dizziness. Three days prior the patient completed an echocardiogram that revealed tricuspid regurgitation with right ventricular dilation and a right ventricular systolic pressure of 116 mmHg. Cardiology was consulted and completed right heart catheterization, VQ scan, as well as autoimmune and infectious investigations. The patient was diagnosed with Portopulmonary Hypertension (PPHTN) complicated by liver cirrhosis. Treatment was initiated with sildenafil, amlodipine, aspirin and continuous oxygen with scheduled outpatient appointments for both IV prostacyclin treatment and pre-liver transplant (LT) evaluation.

Keywords:
Portopulmonary hypertension cardiology cirrhosis pulmonary

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