A Composite Pheochromocytoma-ganglioneuroma: A Case Report

Fatma Mnif^1, , Asma Zargni¹, Dhoha Ben Salah¹, Mouna Mnif Feki¹, Nabila Rekik¹ and Mohamed Abid¹

¹Department of Endocrinology, Hedi Chaker University Hospital, Sfax, Tunisia

Cite this paper:
Fatma Mnif, Asma Zargni, Dhoha Ben Salah, Mouna Mnif Feki, Nabila Rekik and Mohamed Abid. A Composite Pheochromocytoma-ganglioneuroma: A Case Report. American Journal of Medical Case Reports. 2019; 7(12):308-310. doi: 10.12691/ajmcr-7-12-2

Abstract

Composite pheochromocytomas are considered rare neoplasms of the adrenal gland. We report a case of composite pheochromocytoma in a 53-year-old woman, with a 4-year medical history of uncontrolled hypertension without hypokalemia and treated with three antihypertensive. A computed tomographic scan was performed, showing the presence of a spontaneously hypodense adrenal mass of 6 x 6 x 3 cm at the expense of the outer arm of the right adrenal gland, and with microcalcifications and a double component. Laboratory studies showed elevated urinary metanephrines. Diagnosis of pheochromocytoma was retained. The patient underwent surgery and pathologic examination concluded the presence of a composite pheochromocytoma.

Keywords:
hypertension hypokalemia adrenal gland composite pheochromocytoma ganglioneuroma

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