American Journal of Medical Case Reports. 2019, 7(8), 170-172
DOI: 10.12691/ajmcr-7-8-5
Open AccessCase Report
Salem Bouomrani1, 2, , Rim Mesfar1, 2, Moez BenAyed2, 3, Mouna Guermazi1, 2, Hassène Baïli1 and Souad Yahyaoui1
1Department of Internal Medicine, Military Hospital of Gabes, Gabes 6000, Tunisia
2Sfax Faculty of Medicine, University of Sfax, Sfax 3029, Tunisia
3Department of Orthopedics, Regional Hospital of Gabes, Gabes 6000, Tunisia
Pub. Date: July 11, 2019
Cite this paper:
Salem Bouomrani, Rim Mesfar, Moez BenAyed, Mouna Guermazi, Hassène Baïli and Souad Yahyaoui. Juvenile Dermatomyositis Associated to Familial Mediterranean Fever. American Journal of Medical Case Reports. 2019; 7(8):170-172. doi: 10.12691/ajmcr-7-8-5
Abstract
Familial Mediterranean Fever (FMF) is a rare hereditary auto-inflammatory disease that can be exceptionally associated with many other dys-immune disorders; the most reported associations were with systemic vasculitis, spondyloarthropathies, inflammatory bowel diseases, systemic lupus erythematous, multiple sclerosis, and juvenile chronic arthritis. The association of FMF with primary inflammatory myopathy remains exceptional and unusual; it has only been noted once before with adult polymyositis. We report an original observation of FMF associated with juvenile dermatomyositis in an eight-year-old boy, which, to our knowledge, has not been reported previously.Keywords:
familial mediterranean fever juvenile dermatomyositis dermatomyositis
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