Karthikeya Patil^1,, Mahima V Guledgud¹, Ankita Sahni¹

Sturge Weber Syndrome is a rare non hereditary congenital sporadic disorder of elusive etiology. It has a vast continuum of cutaneous, neurologic, ophthalmic and oral manifestations. Routine dental procedures are associated with increased jeopardy of hemorrhage making treatment in such patients an exigent task for oral health care practitioners. Untoward complications can be prevented by having profound knowledge of this rare disorder. We report a case of characteristic oral manifestations in Sturge Weber Syndrome along with a review of relevant prevailing literature.

Sturge Weber syndrome, congenital, encephalotrigeminal angiomatosis, vascular lesions, oral manifestations