@article{novn2017211,
author={{Foster, Emma and Monif, Mastura and Mason, Kylie and Walt, Anneke van der},
title={Diagnosis within a Diagnosis: An Unusual Case of Intracranial Hypertension},
journal={Neuro Ophthalmology & Visual Neuroscience},
volume={2},
number={1},
pages={1--3},
year={2017},
url={http://pubs.sciepub.com/novn/2/1/1},
issn={2572-7281},
abstract={A 56 year old man presented with several months of new onset headaches and blurred vision. Lumbar puncture revealed elevated intracranial pressure, but multiple cerebral imaging studies failed to identify a secondary cause. Eventually a formal venogram revealed a transverse venous sinus thrombosis, and an occult malignancy screen led to a diagnosis of non-Langerhans histiocytosis, or Erdheim-Chester Disease. This case highlights two important learning points: 1) secondary causes for raised intracranial pressure should be vigorously sought in atypical cases of idiopathic intracranial hypertension; 2) ECD is a rare but important cause of ophthalmologic and neurologic presentations, and should be a differential for orbital infiltration, intra- and extracranial disease.},
doi={10.12691/novn-2-1-1}
publisher={Science and Education Publishing}
}