eng Science and Education Publishing American Journal of Medical Case Reports 2374-216X 2019-07-11 7 8 170 172 10.12691/ajmcr-7-8-5 AJMCR2019785 article Salem Bouomrani salembouomrani@yahoo.fr 1 2 Rim Mesfar 2 2 Moez BenAyed 2 3 Mouna Guermazi 3 3 Hassène Baïli 3 Souad Yahyaoui 3 Department of Internal Medicine, Military Hospital of Gabes, Gabes 6000, Tunisia Familial Mediterranean Fever (FMF) is a rare hereditary auto-inflammatory disease that can be exceptionally associated with many other dys-immune disorders; the most reported associations were with systemic vasculitis, spondyloarthropathies, inflammatory bowel diseases, systemic lupus erythematous, multiple sclerosis, and juvenile chronic arthritis. The association of FMF with primary inflammatory myopathy remains exceptional and unusual; it has only been noted once before with adult polymyositis. We report an original observation of FMF associated with juvenile dermatomyositis in an eight-year-old boy, which, to our knowledge, has not been reported previously. http://pubs.sciepub.com/ajmcr/7/8/5/ajmcr-7-8-5.pdf familial mediterranean fever juvenile dermatomyositis dermatomyositis