eng Science and Education Publishing American Journal of Medical Case Reports 2374-216X 2018-08-23 6 8 157 160 10.12691/ajmcr-6-8-3 AJMCR2018683 article Pramod Theetha Kariyanna 1 Apoorva Jayarangaiah 2 Abdullah Mahmood 3 Mitchell Hare 4 Nicholas Taklalsingh 4 Isabel M. McFarlane Isabel.mcfarlane@downstate.edu 4 Divisions of Cardiovascular Disease and Rheumatology, Department of Internal Medicine, State University of New York, Downstate Medical Center, Brooklyn, New York, U.S.A- 11203 Department of Internal Medicine, Wake Forest University, Baptist Health Care System, Winston-Salem, North Carolina, U.S.A- 27157 Department of Internal Medicine, Brookdale University Hospital and Medical Center, Brooklyn, New York, U.S.A- 11212 Ross University School of Medicine, Portsmouth, Dominica Idiopathic inflammatory myopathy (IIM) is a rare autoimmune myopathy that includes polymyositis, dermatomyositis, inclusion body myositis and autoimmune necrotizing myositis. Cardiac involvement was considered a rare occurrence in IIM however, recent reports suggests that cardiac involvement is a common feature and portends poor prognosis as it is usually encountered in advanced disease. IIM leads to myocarditis with subsequent development of myocardial fibrosis, cardiac conduction system disease and cardiomyopathy resulting in both systolic and diastolic heart failure. Conduction abnormalities such as first, second and third degree atrioventricular blocks, right and left bundle branch blocks associated with IIM have been reported. We present a case of a 44-year-old woman with biopsy proven-IIM whose left ventricular ejection fraction (LVEF) and electrocardiogram (ECG) were recorded as normal two years prior. On presentation to our hospital ECG revealed atrial tachycardia and 2D echocardiogram revealed heart failure with reduced ejection fraction (20-30%). Patient quickly progressed to complete heart block. A cardiac resynchronization therapy-defibrillator (CRT-D) insertion was planned but patient succumbed to sepsis. http://pubs.sciepub.com/ajmcr/6/8/3/ajmcr-6-8-3.pdf idiopathic inflammatory myopathy atrial tachycardia heart failure with reduced ejection fraction