eng Science and Education Publishing American Journal of Medical Case Reports 2374-216X 2018-02-01 6 1 12 14 10.12691/ajmcr-6-1-4 AJMCR2018614 article Stefan Rodic srodic@uwo.ca 1 Richard Dunbar-Yaffe 2 Schulich School of Medicine, Western University, London, Canada Division of General Internal Medicine, University of Toronto, Toronto, Canada Herein, we present a case of limited granulomatosis with polyangiitis (GPA) with ocular/aural involvement and sparing of the visceral organs. This atypical constellation of symptoms was initially thought to have an infectious cause prior to repeat imaging and testing of immunological markers. The patient was of African-Caribbean descent, a population where the incidence of granulomatosis with polyangiitis is exceedingly uncommon. This case highlights a unique variant of GPA and emphasizes the importance of early clinical detection and treatment to prevent associated morbidity and mortality. http://pubs.sciepub.com/ajmcr/6/1/4/ajmcr-6-1-4.pdf granulomatosis polyangiitis vasculitis GPA ocular aural ANCA