Science and Education Publishing American Journal of Cancer Prevention 2328-7314 5 1 2017 3 14 Extranuchal-type Fibroma Mimicking Low Grade Sarcoma: A Case Report and Review of the Literature 17 20 EN Mazaher Ramezani Marziyeh Masnadjam Masoud Sadeghi Medical Biology Research Center, Kermanshah University of Medical Sciences, Kermanshah, Iran AJCP2017513 10.12691/ajcp-5-1-3 2016 10 19 2017 2 11 2017 3 12 Nuchal-type fibroma (NTF) is a rare fibrous growth that developing in the nuchal region, in some instances it occurs at the extranuchal sites. Herein, this study reported a case of NTF on extranuchal site in an Iranian girl in Western Iran. The report included a 14-year-old girl with a chief complaint of right hemithorax suprascapular soft tissue mass since 6 years ago and tenderness since last month that physical examination showed firm, tender, non-erythematous mass measuring 5x10 cm with adhesion to surrounding tissue was noted on the right hemithorax over the scapula. Frozen section diagnosis showed spindle cell tumor compatible with low grade sarcoma, but the pathologist reported an extranuchal-type fibroma in permanent. In conclusion, NTF occurs more frequently in middle-aged adults and is more common in men. The prevalence of nuchal region is more than extranuchal region in NTF patients. The NTF is associated with trauma more than Gardner's syndrome. Also, the pathologist and surgeon must be aware of this entity, especially at extranuchal sites, not to be misinterpreted as sarcoma.