Global Journal of Surgery
ISSN (Print): 2379-8742 ISSN (Online): 2379-8750 Website: http://www.sciepub.com/journal/js Editor-in-chief: Baki Topal
Open Access
Journal Browser
Go
Global Journal of Surgery. 2013, 1(1), 1-3
DOI: 10.12691/js-1-1-1
Open AccessCase Report

Primary Retroperitoneal Mucinous Cystadenoma with Sarcomatous Carcinoma in Mural Nodule

Ramia JM, , De la Plaza R, Arteaga V, Adel F, Valenzuela J and Garcia-Parreño J

Pub. Date: March 09, 2013

Cite this paper:
Ramia JM, De la Plaza R, Arteaga V, Adel F, Valenzuela J and Garcia-Parreño J. Primary Retroperitoneal Mucinous Cystadenoma with Sarcomatous Carcinoma in Mural Nodule. Global Journal of Surgery. 2013; 1(1):1-3. doi: 10.12691/js-1-1-1

Abstract

Primary retroperitoneal mucinous cystic tumors are extremely rare neoplasms that usually occur in women. Their histogenesis has not been clarified. Their low incidence has meant that it difficult to define therapeutic strategies or prognosis, or to record survival data. We describe a 35 year-old female with a retroperitoneal mucinous cystadenoma presenting a mural nodule with foci of sarcomatoid carcinoma. The entire tumor was surgically removed. After surgery, the patient received six cycles of carboplatin and paclitaxel. After 30 months of follow up she has shown no signs of recurrence. We review the etiology, diagnosis and therapeutic options in these extremely rare tumors.

Keywords:
retroperitoneal tumor surgery mucinous cystic sarcomatoid review

Creative CommonsThis work is licensed under a Creative Commons Attribution 4.0 International License. To view a copy of this license, visit http://creativecommons.org/licenses/by/4.0/

Figures

Figure of 3

References:

[1]  Roma A, Malpica A. Primary retroperitoneal mucinous tumors: a clinicopathologic study of 18 cases. Am J Surg Pathol 2009; 33: 526-532.
 
[2]  Cantú D, Perez-Montiel D, Chanona J, Dueñas A, Villavicencio V, Zavala G. Primary retroperitoneal mucinous cystoadencoarcinomas: report of two cases. World J Surg Oncol 2007; 5: 5-11
 
[3]  Suzuki S, Mishina T, Ishizuka D, Fukase M, Matsubara Y. Mucinous cystoadenocarcinoma of the retroperitoneum: report of a case. Surg Today 2001; 31:747-750
 
[4]  Min BW, Kim JM, Um JW, Lee ES, Son GS, Kim SJ, Moon HY. The first case of primary retroperitoneal mucinous cystadenoma in Korea: a case report. Korean J Int Med 2004; 19:282-284.
 
[5]  Moral M, García-Blanch G, Sánchez A, Díaz G, Cuberes R. Cistoadenoma mucinoso retroperitoneal primario. Cir Esp 2008; 84:165-175.
 
[6]  Yang DM, Jung DH, Kim H, Kang JH, Kim SH, Kim JH, Hwang HY. Retroperitoneal cystic masses; CT, clinical and patholigical findings and literature review. Radiographics 2004; 24: 1353-1365.
 
[7]  Bakker RFR, Stoot JHMB, Blok P, Merkus JWS. Primary retroperitoneal mucinous cystoadenoma with sarcoma-like mural nodule. Virchows Arch 2007; 451:853-857.
 
[8]  Chen JS, Lee WJ, Chang YJ, Wu MZ, Chiu KM Laparoscopic resecton of a primary retroperitoneal mucinous cystoadenoma: report of a case. Surg Today 1998; 28:343-345.
 
[9]  Kessler TM, Kessler W, Neuweiler J, Nachbur H. Treatment of a case of primary retroperitoneal mucinous cystoadenocarcinoma: is adjuvant hysterectomy and bilateral salpingo-oopherectomy justified? Am J Obstet Gynecol 2002; 187:227-232.
 
[10]  Navin P, Meshkat B, mcHugh S, beegan C, Leen E, Prins H, Aly S. Primary retroperitoneal mucinous cystadenoma. A case study and review of the literature. Int J Surg Case Reports 2012; 3:486-488
 
[11]  Falidas E, Konstandoudakis S, Vlachos K, Archontovasilis F, Mathioulakis S, Boutzouvis S, Villias C Primary retroperitoneal mucinous cystadenoma of borderline malignancy in a male patient. Case report and review of the literature World J Surg Oncol 2011; 9:98-102