American Journal of Medical Case Reports
ISSN (Print): 2374-2151 ISSN (Online): 2374-216X Website: http://www.sciepub.com/journal/ajmcr Editor-in-chief: Samy, I. McFarlane
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American Journal of Medical Case Reports. 2018, 6(10), 193-201
DOI: 10.12691/ajmcr-6-10-1
Open AccessCase Report

A Dento – Surgical Management of a Cleidocranial Dysplasia Case. A New Approach for Better Oral Health Quality of Life Part II to: (A 9-year-old Saudi Boy with Cliedocranial Dysplasia)

Rabab A. Al Buainain1, Tarek Ezzeldin2, Hoda Abougareeb3, Faisal Al Sineedi4, Basma A. Almaghlouth5, Yousef H. Almoumen6 and Abdullah Faraj Alshammari7,

1Senior Resident in Saudi Board Pediatric Dentistry Program, Dammam Medical Complex, Ministry of Health, Kingdom of Saudi Arabia

2Consultant in Pediatric Dentistry, (French Board Certified) Dammam Medical Complex, Ministry of Health, Kingdom of Saudi Arabia

3Consultant in Pediatric Dentistry, Dammam Medical Complex, Ministry of Health, Kingdom of Saudi Arabia

4Consultant in Pediatric Dentistry, King Fahad Military Medical Complex, Ministry of Defense, Kingdom of Saudi Arabia

5SBO Consultant in Orthodontics, Dammam Medical Complex, Ministry of Health, Kingdom of Saudi Arabia

6Consultant in Oral & Maxillo Facial Surgery, BDS, SBOMFS, AAAM (American Academy of Aesthetic Medicine Board Certified)

7College of Dentistry, University of Hail, Hail, KSA

Pub. Date: October 23, 2018

Cite this paper:
Rabab A. Al Buainain, Tarek Ezzeldin, Hoda Abougareeb, Faisal Al Sineedi, Basma A. Almaghlouth, Yousef H. Almoumen and Abdullah Faraj Alshammari. A Dento – Surgical Management of a Cleidocranial Dysplasia Case. A New Approach for Better Oral Health Quality of Life Part II to: (A 9-year-old Saudi Boy with Cliedocranial Dysplasia). American Journal of Medical Case Reports. 2018; 6(10):193-201. doi: 10.12691/ajmcr-6-10-1

Abstract

Background: Cleidocranial dysplasia is a rare congenital defect of autosomal dominant heritable disease with prevalence of 1 per 1,000000 individuals. It is primarily affects bones which undergo intramembranous ossification [1,2,3,4]. Case presentation: A 9 years old Saudi male with CCD attended Pediatric Dental Clinics in Dammam Medical Complex. Chief complaint was delay eruption of permanent teeth and multiple caries. Based on clinical examination, radiographic investigations including CBCT & with coordination between Pediatric Dentistry, maxillofacial surgery and Orthodontic departments, a treatment plan has been concluded taking into consideration the wellbeing and the oral health related life style of the patient by addressing a new approach to preserve all the primary teeth, surgically removing all supernumerary teeth, applying removal or fixed modified Gropers’ appliance to improve speech, esthetic & function than observing the eruption of the permanent teeth to intervene orthodontically only when needed. Conclusion: Team work involving multi-disciplinary departments helped to select a preeminent & new dental management approach for CCD patients including all aspects needed, Dental rehabilitation, Surgical & Orthodontic treatment to provide better oral health quality of life for the young patient.

Keywords:
cliedocranial dysplasia dammam approach oral health quality of life dento-surgical management

Creative CommonsThis work is licensed under a Creative Commons Attribution 4.0 International License. To view a copy of this license, visit http://creativecommons.org/licenses/by/4.0/

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