American Journal of Medical Case Reports
ISSN (Print): 2374-2151 ISSN (Online): 2374-216X Website: http://www.sciepub.com/journal/ajmcr Editor-in-chief: Apply for this position
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American Journal of Medical Case Reports. 2018, 6(2), 21-23
DOI: 10.12691/ajmcr-6-2-2
Open AccessCase Report

Clival Chordoma in Children a Rare Condition: Case Report

Ali Al Mashni1, Neeraj Salhotra1, , Mohammad Hadad1, Mohammad Hashim1, Tariq Al Saidi1 and Samit Biniwal1

1Neurosurgeon Khoula Hospital Muscat Oman

Pub. Date: March 07, 2018

Cite this paper:
Ali Al Mashni, Neeraj Salhotra, Mohammad Hadad, Mohammad Hashim, Tariq Al Saidi and Samit Biniwal. Clival Chordoma in Children a Rare Condition: Case Report. American Journal of Medical Case Reports. 2018; 6(2):21-23. doi: 10.12691/ajmcr-6-2-2

Abstract

A three year child had presented to our OPD with complaints of nasal obstruction, change of voice and difficulty in ingestion. Patient was investigated and was seen having a mass in the nasopharynx. Further investigations revealed on CT and MRI brain a large tumour destroying the clival region with nasopharyngeal and intracranial extension with pressure effect on brain stem and lower cranial nerves. Patient underwent two stage surgery retromastoid craniectomy with excision of intracranial part and later a tracheostomy and transoral excision of the nasopharyngeal extension and part anterior to brain stem. Patient made a remarkable recovery and was discharged home after tracheostomy removal with advice to follow with pediatric oncology for chemotherapy as HPE revealed it to be clival chordoma a rare entity in children.

Keywords:
clival chordoma in children

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