American Journal of Medical Case Reports
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American Journal of Medical Case Reports. 2018, 6(1), 12-14
DOI: 10.12691/ajmcr-6-1-4
Open AccessCase Report

A unique Presentation of Granulomatosis with Polyangiitis in a Patient of African-Caribbean Descent

Stefan Rodic1, and Richard Dunbar-Yaffe2

1Schulich School of Medicine, Western University, London, Canada

2Division of General Internal Medicine, University of Toronto, Toronto, Canada

Pub. Date: February 01, 2018

Cite this paper:
Stefan Rodic and Richard Dunbar-Yaffe. A unique Presentation of Granulomatosis with Polyangiitis in a Patient of African-Caribbean Descent. American Journal of Medical Case Reports. 2018; 6(1):12-14. doi: 10.12691/ajmcr-6-1-4


Herein, we present a case of limited granulomatosis with polyangiitis (GPA) with ocular/aural involvement and sparing of the visceral organs. This atypical constellation of symptoms was initially thought to have an infectious cause prior to repeat imaging and testing of immunological markers. The patient was of African-Caribbean descent, a population where the incidence of granulomatosis with polyangiitis is exceedingly uncommon. This case highlights a unique variant of GPA and emphasizes the importance of early clinical detection and treatment to prevent associated morbidity and mortality.

granulomatosis polyangiitis vasculitis GPA ocular aural ANCA

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