American Journal of Medical Case Reports
ISSN (Print): 2374-2151 ISSN (Online): 2374-216X Website: Editor-in-chief: Samy, I. McFarlane
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American Journal of Medical Case Reports. 2015, 3(11), 347-351
DOI: 10.12691/ajmcr-3-11-1
Open AccessCase Report

A Rapidly Growing Pseudoaneurysm Secondary to Aortic Arch Periaortitis

Rong-Hsin Yang1, Chien-Hsin Ting1 and Yum-Kung Chu1,

1Department of Nuclear Medicine, Taipei Veterans General Hospital, Taipei, Taiwan

Pub. Date: September 24, 2015

Cite this paper:
Rong-Hsin Yang, Chien-Hsin Ting and Yum-Kung Chu. A Rapidly Growing Pseudoaneurysm Secondary to Aortic Arch Periaortitis. American Journal of Medical Case Reports. 2015; 3(11):347-351. doi: 10.12691/ajmcr-3-11-1


We herein report a case of rapidly growing pseudoaneurysm developed shortly after a diagnosis of aortic arch periaortitis. Pseudoaneurysm is a blood leak constrained by compliance of perivascular tissues, in persistent communication with the feeding artery. Chronic periaortitis is characterized by inflammatory involvement of the outer layer of the aorta and surrounding tissues. The major pathogenetic process leading to periaortitis is inflammation, caused by advanced atherosclerosis. Autoimmunity has been proposed as a contributing factor. The present case illustrates an ongoing process of aortic arch periaortitis toward aneurysm formation. Aortic arch pseudoaneurysm is highly susceptible to rupture and sudden death. Our patient achieved a complete remission by a month after receiving an endovascular stent repair and combined treatment with steroid and antibiotics. The disease process was documented by serial CT and radionuclide scanning.

aortic arch atherosclerosis computed tomography Ga-67 scan periaortitis pseudoaneurysm

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