American Journal of Medical Case Reports
ISSN (Print): 2374-2151 ISSN (Online): 2374-216X Website: http://www.sciepub.com/journal/ajmcr Editor-in-chief: Samy, I. McFarlane
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American Journal of Medical Case Reports. 2015, 3(3), 53-58
DOI: 10.12691/ajmcr-3-3-1
Open AccessCase Report

Coarctation of Aorta with Supravalvular Pulmonary Stenosis in an Adult Patient: A Rare Exception of the Fetal Flow Pattern Theory

Manish Ruhela1, , Harneesh Randhawa1, Prachi Bagarhatta2, Rajeev Bagarhatta1 and Anoop Jain1

1Department of Cardiology, Sawai Man Singh Medical College and Hospital, Jaipur, Rajasthan, India

2Lady Hardinge Medical College, New Delhi, India

Pub. Date: January 28, 2015

Cite this paper:
Manish Ruhela, Harneesh Randhawa, Prachi Bagarhatta, Rajeev Bagarhatta and Anoop Jain. Coarctation of Aorta with Supravalvular Pulmonary Stenosis in an Adult Patient: A Rare Exception of the Fetal Flow Pattern Theory. American Journal of Medical Case Reports. 2015; 3(3):53-58. doi: 10.12691/ajmcr-3-3-1

Abstract

Coarctation of the aorta is a common congenital defect whose overall incidence is 5–8% of all congenital cardiac anomalies. Associated cardiac anomalies have been well described in previous studies examining specific subgroups of coarctation of aorta patients, particularly infants, excluding older children, adolescents, and adults. The association of coarctation with left-sided obstructive lesions ( Bicuspid aortic valve, Parachute mitral valve, Mitral atresia, Aortic atresia ) were well documented in the literature. The association of coarctation of aorta with right- sided obstructive lesions is rare and a hemodyanamic explanation based on fetal flow pattern was given for this. Herein we report a case of coarctation of aorta with right sided obstructive lesion in form of supravalvular pulmonary stenosis in an adult female. To the best of our knowledge this is the first case report where an adult female presented with coarctation of aorta along with supravalvular pulmonary stenosis.

Keywords:
coarctation of aorta supravalvular pulmonary stenosis fetal flow pattern theory

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