American Journal of Medical Case Reports
ISSN (Print): 2374-2151 ISSN (Online): 2374-216X Website: Editor-in-chief: Samy, I. McFarlane
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American Journal of Medical Case Reports. 2015, 3(2), 40-41
DOI: 10.12691/ajmcr-3-2-6
Open AccessCase Report

Systemic Lupus Erythematosus Revealing Splenic Marginal Zone Lymphoma. A Case Report

Bel Feki N1, , Smiti Khanfir M1, Said F1, Hamzaoui A1, Ben Salem T1, Ben Ghorbel I1, Lamloum M1, Ben Romdhane N1 and Houman MH1

1Internal Medicine Department. University hospital of La Rabta, Tunis. Tunisia

Pub. Date: January 23, 2015

Cite this paper:
Bel Feki N, Smiti Khanfir M, Said F, Hamzaoui A, Ben Salem T, Ben Ghorbel I, Lamloum M, Ben Romdhane N and Houman MH. Systemic Lupus Erythematosus Revealing Splenic Marginal Zone Lymphoma. A Case Report. American Journal of Medical Case Reports. 2015; 3(2):40-41. doi: 10.12691/ajmcr-3-2-6


Autoimmune manifestations are common in splenic marginal zone lymphoma (SMZL) and are sometimes the presenting feature of the disease. We report Herein the case of a 72-year old woman presenting with systemic lupus erythematosus revealing SMZL. To our knowledge, there are only 3 case reports of SLE associated to SMZL. In case of authentic autoimmune disease with unusual clinical features Physician awareness is recommended, to rule out associated lymphoproliferative syndrome.

systemic lupus erythematosus splenic marginal zone lymphoma

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