American Journal of Medical Case Reports
ISSN (Print): 2374-2151 ISSN (Online): 2374-216X Website: http://www.sciepub.com/journal/ajmcr Editor-in-chief: Samy, I. McFarlane
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American Journal of Medical Case Reports. 2014, 2(11), 259-261
DOI: 10.12691/ajmcr-2-11-10
Open AccessCase Report

Postinflammatory Cutis Laxa: A Case Report

Derbali F1, , Hajji R1, Mohamed M2, Mnafgui K3, Hammedi F4, Elleuch M1, Kammoun N1 and Zribi S1

1Internal Medicine Department, Sidi Bouzid Regional Hospital, Sidi Bouzid, Tunisia

2Dermatology Department, Monastir University Hospital, Monastir, Tunisia

3Pathophysiology department, FSS, Sfax, Tunisia

4Pathology Department, Monastir University Hospital, Monastir, Tunisia

Pub. Date: November 20, 2014

Cite this paper:
Derbali F, Hajji R, Mohamed M, Mnafgui K, Hammedi F, Elleuch M, Kammoun N and Zribi S. Postinflammatory Cutis Laxa: A Case Report. American Journal of Medical Case Reports. 2014; 2(11):259-261. doi: 10.12691/ajmcr-2-11-10

Abstract

Cutis Laxa (CL) is a rare disease in which the skin loses its elasticity and hangs in large folds. It is an inherited or acquired connective tissue disorder. We report the case of a 29 year-old woman followed up since 4 years for a dermatomyositis treated with glucocorticosteroids and methotrexate. She was hospitalized in February 2012 for fever, arthralgia, pelvic and shoulder muscle weakness with myalgia, malar rash, thrombocytopenia, leucopenia and lymphocytopenia Immunological tests showed Antinuclear Antibodies (ANA) (+) to 1/640, AC anti-DNA (+) and AC anti-SSA (+). Histology of the salivary glands showed grade III lymphocytic sialadenitis. The systemic lupus erythematosus and secondary Sjögren’s syndrome were diagnosed. The patient was treated with glucocorticostroids, methotrexate, nivaquine and bissolvon. One year later, the patient presented a skin aging that began in hands which has expanded rapidly in the face. The skin biopsy confirmed the diagnosis of a "Cutis Laxa". The esthetic treatment is proposed.

Keywords:
Acquired cutis laxa systemic disease systemic lupus erythematosus dermatomyositis Sjögren’s syndrome

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