American Journal of Medical Case Reports
ISSN (Print): 2374-2151 ISSN (Online): 2374-216X Website: Editor-in-chief: Samy, I. McFarlane
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American Journal of Medical Case Reports. 2020, 8(8), 253-256
DOI: 10.12691/ajmcr-8-8-11
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Quadricuspid Aortic Valve: A Case Report and Review

Pramod Theetha Kariyanna1, Jonathan Francois1, Amog Jayarangaiah2, Yuvraj Singh Chowdhury1, Richard Grodman3, Moro O. Salifu1 and Isabel M. McFarlane1,

1Department of Internal Medicine, State University of New York, Downstate Medical Center, Brooklyn NY 11203, USA

2Trinity School of Medicine, Ratho Mill, Ribishi, St. Vincent and Grenadines

3Richmond University Medical Center, Department of Cardiology, Staten Island, New York, United States

Pub. Date: May 18, 2020

Cite this paper:
Pramod Theetha Kariyanna, Jonathan Francois, Amog Jayarangaiah, Yuvraj Singh Chowdhury, Richard Grodman, Moro O. Salifu and Isabel M. McFarlane. Quadricuspid Aortic Valve: A Case Report and Review. American Journal of Medical Case Reports. 2020; 8(8):253-256. doi: 10.12691/ajmcr-8-8-11


Quadricuspid aortic valve (QAV) is a rare congenital valvular abnormality with less than 200 cases reported to date. The first QAV was reported in 1862 by Balington. Clinical manifestations of patients with a QAV depend on the functional status of the QAV and the associated cardiac disorders. Most QAV are asymptomatic and are incidentally found. Severe aortic regurgitation and/or stenosis can develop overtime, requiring aortic valve replacement or repair. Transesophageal echocardiography is the preferred modality to diagnose QAV. We present a case of QAV which was incidentally diagnosed in a 43-year-old woman who presented with gastroenteritis.

Quadricuspid aortic valve congenital variant of aortic valve Hurwitz and Robert’s classification

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