American Journal of Cancer Prevention
ISSN (Print): 2328-7314 ISSN (Online): 2328-7322 Website: http://www.sciepub.com/journal/ajcp Editor-in-chief: Nabil Abdel-Hamid
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American Journal of Cancer Prevention. 2013, 1(3), 24-26
DOI: 10.12691/ajcp-1-3-2
Open AccessCase Report

Pancreatic Ewings Sarcoma- A Dreadful Tumor

Kumar Jayant1, , Swati Agrawal2, Rajendra Agarwal3 and Susheela Khoiwal4

1Department of Surgery, Sudha Hospital &Medical Research Centre, Talwandi, Kota, Rajasthan, India

2Sudha Hospital & Medical Research Centre Kota, Rajasthan, India

3Head of Dept of Surgery, Sudha Hospital &Medical Research Centre Kota, Rajasthan, India

4Department of Obs & Gynae, RNT Medical College, Udaipur

Pub. Date: December 22, 2013

Cite this paper:
Kumar Jayant, Swati Agrawal, Rajendra Agarwal and Susheela Khoiwal. Pancreatic Ewings Sarcoma- A Dreadful Tumor. American Journal of Cancer Prevention. 2013; 1(3):24-26. doi: 10.12691/ajcp-1-3-2

Abstract

Extraosseous Ewing’s sarcoma/primitive neuroectodermal tumor (ES/PNET) is an uncommon, aggressive, and malignant tumor with poor outcome. Pancreas in one of the very rare extraosseous location for this tumor thus minimal information regarding this disorder is present in literature. The present case was clinically and radiologically misdiagnosed as a pancreatic tumor. Histopathology of the tumor tissue revealed “small round cells” that were positive for CD99 (MIC-2), confirming the diagnosis of ES/PNET. This case report emphasis on the importance of considering Ewing’s sarcoma in the differential diagnosis of intraabdominal, extraintestinal masses particularly in young patients presenting with pancreatic mass.

Keywords:
extraosseous ewing’s sarcoma pancreatic carcinoma atypical pancreatic carcinoma primitive neuroectodermal tumor

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